Beginning in mid-February 2008, the 1997-2007 online version of the Science Watch® newsletter, ESI-Topics.com, and in-cites.com, will all be featured together on the redesigned ScienceWatch.com. All previous content from the three sites will be permanently archived, and remain accessible from any existing bookmarks to the archived pages. No new content will be added to this site. Updates and new content (updated biweekly) are available at ScienceWatch.com now.
Thomson
Essential Science Indicators - Special Topics  RSS feeds for the editorial Web sites of Essential Science Indicators.
All Topics Menu
Help || About || Contact

  
|  Previous Page  |
  |  Special Topics Menu  |  |  Next Page  |
  

ESI Special Topic of:
"Mad Cow & Other Prion Diseases," Published August 2003

•> Search Special Topics
Mad Cow & Other Prion Diseases Menu

Mad Cow & Other Prion Diseases
& Other Prion Diseases

TOP PAPERS

  • Top 20 papers overall

  
***Article 1
Total Cites: 858
Article Title: A NEW VARIANT OF CREUTZFELDT-JAKOB DISEASE IN THE UK
Authors: Will, RG, Ironside, JW, Zeidler, M, Cousens, SN, Estibeiro, K, Alperovitch, A, Poser, S, Pocchiari, M, Hofman, A, Smith, PG
Journal: LANCET
Volume: 347
Page: 921-925
Year: 1996
Addresses: 
· WESTERN GEN HOSP, NATL CJD SURVEILLANCE UNIT, EDINBURGH EH4 2XU, MIDLOTHIAN, SCOTLAND
· LONDON SCH HYG & TROP MED, DEPT EPIDEMIOL & POPULAT SCI, LONDON WC1, ENGLAND
· HOP LA PITIE SALPETRIERE, INSERM, PARIS, FRANCE
· UNIV GOTTINGEN, NEUROL KLIN & POLIKLIN, W-3400 GOTTINGEN, GERMANY
· IST SUPER SANITA, VIROL LAB, I-00161 ROME, ITALY
· ERASMUS UNIV ROTTERDAM, ROTTERDAM, NETHERLANDS

***Article 2
Total Cites: 564
Article Title: MOLECULAR ANALYSIS OF PRION STRAIN VARIATION AND THE AETIOLOGY OF 'NEW VARIANT' CJD
Authors: Collinge, J, Sidle, KCL, Meads, J, Ironside, J, Hill, AF
Journal: NATURE
Volume: 383
Page: 685-690
Year: 1996
Addresses: 
· ST MARYS, IMPERIAL COLL SCH MED, DEPT BIOCHEM & MOL GENET, NEUROGENET UNIT, LONDON W2 1PG, ENGLAND
· WESTERN GEN HOSP, NATL CJD SURVEILLANCE UNIT, EDINBURGH EH4 2XU, MIDLOTHIAN, SCOTLAND
· ST MARYS HOSP, DEPT NEUROL, LONDON W2 1NY, ENGLAND

***Article 3
Total Cites: 540
Article Title: PRIONS
Authors: Prusiner, SB
Journal: PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
Volume: 95
Page: 13363-13383
Year: 1998
Addresses: 
· Univ Calif San Francisco, Dept Neurol, San Francisco, CA, USA
· Univ Calif San Francisco, Dept Neurol, San Francisco, CA, USA
· Univ Calif San Francisco, Dept Biochem & Biophys, San Francisco, CA, USA

***Article 4
Total Cites: 496
Article Title: TRANSMISSIONS TO MICE INDICATE THAT 'NEW VARIANT' CJD IS CAUSED BY THE BSE AGENT
Authors: Bruce, ME, Will, RG, Ironside, JW, Mcconnell, I, Drummond, D, Suttie, A, Mccardle, L, Chree, A, Hope, J, Birkett, C, Cousens, S, Fraser, H, Bostock, CJ
Journal: NATURE
Volume: 389
Page: 498-501
Year: 1997
Addresses: 
· INST ANIM HLTH, BBSRC MRC NEUROPATHOGENESIS UNIT, W MAINS RD, EDINBURGH EH9 3JF, MIDLOTHIAN, SCOTLAND
· WESTERN GEN HOSP, NATL CJD SURVEILLANCE UNIT, EDINBURGH EH4 2XU, MIDLOTHIAN, SCOTLAND
· INST ANIM HLTH, NEWBURY RG20 7NN, BERKS, ENGLAND
· UNIV LONDON LONDON SCH HYG & TROP MED, DEPT EPIDEMIOL & POPULAT SCI, LONDON WC1E 7HT, ENGLAND

***Article 5
Total Cites: 313
Article Title: PRION PROTEIN IS NECESSARY FOR NORMAL SYNAPTIC FUNCTION
Authors: Collinge, J, Whittington, MA, Sidle, KCL, Smith, CJ, Palmer, MS, Clarke, AR, Jefferys, JGR
Journal: NATURE
Volume: 370
Page: 295-297
Year: 1994
Addresses: 
· ST MARYS HOSP, SCH MED, DEPT BIOCHEM & MOLEC GENET, PRION DIS GRP, LONDON W2 1PG, ENGLAND
· ST MARYS HOSP, SCH MED, DEPT PHYSIOL & BIOPHYS, LONDON W2 1PG, ENGLAND
· ST MARYS HOSP, DEPT NEUROL, LONDON W2 1NY, ENGLAND
· UNIV BRISTOL, SCH MED SCI, DEPT BIOCHEM, BRISTOL BS8 1TD, ENGLAND

***Article 6
Total Cites: 306
Article Title: NMR STRUCTURE OF THE MOUSE PRION PROTEIN DOMAIN PRP(121-231)
Authors: Riek, R, Hornemann, S, Wider, G, Billeter, M, Glockshuber, R, Wuthrich, K
Journal: NATURE
Volume: 382
Page: 180-182
Year: 1996
Addresses: 
· ETH HONGGERBERG, INST MOLEK BIOL & BIOPHYS, CH-8093 ZURICH, SWITZERLAND

***Article 7
Total Cites: 305
Article Title: THE CELLULAR PRION PROTEIN BINDS COPPER IN VIVO
Authors: Brown, DR, Qin, KF, Herms, JW, Madlung, A, Manson, J, Strome, R, Fraser, PE, Kruck, T, Vonbohlen, A, Schulzschaeffer, W, Giese, A, Westaway, D, Kretzschmar, H
Journal: NATURE
Volume: 390
Page: 684-687
Year: 1997
Addresses: 
· UNIV GOTTINGEN, DEPT NEUROPATHOL, D-37075 GOTTINGEN, GERMANY
· UNIV TORONTO, CTR RES NEURODEGENERAT DIS, TORONTO, ON M5S 3H2, CANADA
· UNIV TORONTO, DEPT LAB MED & PATHOBIOL, TORONTO, ON M5S 3H2, CANADA
· UNIV TORONTO, DEPT MED BIOPHYS, TORONTO, ON M5S 3H2, CANADA
· UNIV TORONTO, DEPT PHYSIOL, TORONTO, ON M5S 3H2, CANADA
· NEUROPATHOGENESIS UNIT, EDINBURGH EA 3TF, MIDLOTHIAN, SCOTLAND
· INST SPEKTROCHEM & ANGEW SPEKTROSKOPIE, D-44013 DORTMUND, GERMANY

***Article 8
Total Cites: 286
Article Title: PRION DISEASES AND THE BSE CRISIS
Authors: Prusiner, SB
Journal: SCIENCE
Volume: 278
Page: 245-251
Year: 1997
Addresses: 
· UNIV CALIF SAN FRANCISCO, DEPT NEUROL, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT BIOCHEM & BIOPHYS, SAN FRANCISCO, CA, USA

***Article 9
Total Cites: 245
Article Title: TRANSMISSION DYNAMICS AND EPIDEMIOLOGY OF BSE IN BRITISH CATTLE
Authors: Anderson, RM, Donnelly, CA, Ferguson, NM, Woolhouse, MEJ, Watt, CJ, Udy, HJ, Mawhinney, S, Dunstan, SP, Southwood, TRE, Wilesmith, JW, Ryan, JBM, Hoinville, LJ, Hillerton, JE, Austin, AR, Wells, GAH
Journal: NATURE
Volume: 382
Page: 779-788
Year: 1996
Addresses: 
· UNIV OXFORD, DEPT ZOOL, CTR EPIDEMIOL INFECT DIS, OXFORD OX1 3PS, ENGLAND
· UNIV COLORADO, HLTH SCI CTR, DEPT PREVENT MED & BIOMETR, DENVER, CO, USA
· CENT VET LAB, ADDLESTONE KT15 3NB, SURREY, ENGLAND
· INST ANIM HLTH, COMPTON NG20 7NN, BERKS, ENGLAND

***Article 10
Total Cites: 229
Article Title: ROLE OF MICROGLIA AND HOST PRION PROTEIN IN NEUROTOXICITY OF A PRION PROTEIN FRAGMENT
Authors: Brown, DR, Schmidt, B, Kretzschmar, HA
Journal: NATURE
Volume: 380
Page: 345-347
Year: 1996
Addresses: 
· UNIV GOTTINGEN, INST NEUROPATHOL, D-37075 GOTTINGEN, GERMANY
· UNIV GOTTINGEN, ZENTRUM BIOCHEM & MOL ZELLBIOL, D-37075 GOTTINGEN, GERMANY

***Article 11
Total Cites: 206
Article Title: A CRUCIAL ROLE FOR B CELLS IN NEUROINVASIVE SCRAPIE
Authors: Klein, MA, Frigg, R, Flechsig, E, Raeber, AJ, Kalinke, U, Bluethmann, H, Bootz, F, Suter, M, Zinkernagel, RM, Aguzzi, A
Journal: NATURE
Volume: 390
Page: 687-690
Year: 1997
Addresses: 
· UNIV ZURICH, INST NEUROPATHOL, CH-8091 ZURICH, SWITZERLAND
· UNIV ZURICH, INST MOL BIOL, CH-8091 ZURICH, SWITZERLAND
· UNIV ZURICH, INST EXPT IMMUNOL, CH-8091 ZURICH, SWITZERLAND
· HOFFMANN LA ROCHE AG, CH-4070 BASEL, SWITZERLAND
· UNIV ZURICH, INST LAB ANIM SCI, CH-8057 ZURICH, SWITZERLAND

***Article 12
Total Cites: 197
Article Title: TRANSMISSION OF BOVINE SPONGIFORM ENCEPHALOPATHY AND SCRAPIE TO MICE - STRAIN VARIATION AND THE SPECIES BARRIER
Authors: Bruce, M, Chree, A, Mcconnell, I, Foster, J, Pearson, G, Fraser, H
Journal: PHILOSOPHICAL TRANSACTIONS OF THE ROYAL SOCIETY OF LONDON SERIES B-BIOLOGICAL SCIENCES
Volume: 343
Page: 405-411
Year: 1994
Addresses: 
· AFRC, INST ANIM HLTH, W MAINS RD, EDINBURGH EH9 3JF, MIDLOTHIAN, SCOTLAND
· MRC, NEUROPATHOGENESIS UNIT, EDINBURGH EH9 3JF, MIDLOTHIAN, SCOTLAND
· UNIV BRISTOL, SCH VET SCI, BRISTOL BS18 7DU, AVON, ENGLAND

***Article 13
Total Cites: 194
Article Title: INVESTIGATION OF VARIANT CREUTZFELDT-JAKOB DISEASE AND OTHER HUMAN PRION DISEASES WITH TONSIL BIOPSY SAMPLES
Authors: Hill, AF, Butterworth, RJ, Joiner, S, Jackson, G, Rossor, MN, Thomas, DJ, Frosh, A, Tolley, N, Bell, JE, Spencer, M, King, A, Al-sarraj, S, Ironside, JW, Lantos, PL, Collinge, J
Journal: LANCET
Volume: 353
Page: 183-189
Year: 1999
Addresses: 
· St Marys Hosp, Imperial Coll Sch Med, Dept Neurogenet, Praed St, London W2 1PG, England
· St Marys Hosp, Imperial Coll Sch Med, Dept Neurogenet, London W2 1PG, England
· St Marys Hosp, Specialist Prion Dis Clin, London W2 1PG, England
· St Marys Hosp, Dept Neurol, London W2 1PG, England
· St Marys Hosp, Dept Ear Nose & Throat Surg, London W2 1PG, England
· Natl CJG Surveillance Unit, Edinburgh, Scotland
· Inst Psychiat, Dept Neuropathol, London, England

***Article 14
Total Cites: 171
Article Title: TRANSMISSION OF THE BSE AGENT TO MICE IN THE ABSENCE OF DETECTABLE ABNORMAL PRION PROTEIN
Authors: Lasmezas, CI, Deslys, JP, Robain, O, Jaegly, A, Beringue, V, Peyrin, JM, Fournier, JG, Hauw, JJ, Rossier, J, Dormont, D
Journal: SCIENCE
Volume: 275
Page: 402-405
Year: 1997
Addresses: 
· CEA, SERV NEUROVIROL, DSV, DRM, F-92265 FONTENAY ROSES, FRANCE
· HOP ST VINCENT DE PAUL, INSERM, U29, F-75674 PARIS 14, FRANCE
· HOP LA PITIE SALPETRIERE, INSERM, U153, F-75651 PARIS 13, FRANCE
· HOP LA PITIE SALPETRIERE, INSERM, U360, LAB ESCOUROLLE, F-75651 PARIS 13, FRANCE
· ECOLE SUPER PHYS & CHIM IND VILLE PARIS, CNRS, URA 2054, F-75231 PARIS 5, FRANCE

***Article 15
Total Cites: 159
Article Title: PRION (PRPSC)-SPECIFIC EPITOPE DEFINED BY A MONOCLONAL ANTIBODY
Authors: Korth, C, Stierli, B, Streit, P, Moser, M, Schaller, O, Fischer, R, Schulzschaeffer, W, Kretzschmar, H, Raeber, A, Braun, U, Ehrensperger, F, Hornemann, S, Glockshuber, R, Riek, R, Billeter, M, Wuthrich, K, Oesch, B
Journal: NATURE
Volume: 390
Page: 74-77
Year: 1997
Addresses: 
· UNIV ZURICH, PRION AG, WINTERTHURERSTR 190, CH-8057 ZURICH, SWITZERLAND
· UNIV ZURICH, BRAIN RES INST, CH-8029 ZURICH, SWITZERLAND
· ETH ZURICH, INST BIOCHEM, CH-8092 ZURICH, SWITZERLAND
· UNIV GOTTINGEN, INST NEUROPATHOL, D-37075 GOTTINGEN, GERMANY
· UNIV ZURICH, INST NEUROPATHOL, CH-8091 ZURICH, SWITZERLAND
· UNIV ZURICH, KLIN WIEDERKAUER & PFERDEMED, CH-8057 ZURICH, SWITZERLAND
· UNIV ZURICH, INST VET PATHOL, CH-8057 ZURICH, SWITZERLAND
· ETH ZURICH, INST MOL BIOL & BIOPHYS, CH-8093 ZURICH, SWITZERLAND

***Article 16
Total Cites: 149
Article Title: HUMAN PRION DISEASES
Authors: Prusiner, SB, Hsiao, KK
Journal: ANNALS OF NEUROLOGY
Volume: 35
Page: 385-395
Year: 1994
Addresses: 
· UNIV CALIF SAN FRANCISCO, DEPT NEUROL, HSE 781, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT BIOCHEM & BIOPHYS, SAN FRANCISCO, CA, USA
· UNIV MINNESOTA, DEPT NEUROL, MINNEAPOLIS, MN, USA

***Article 17
Total Cites: 140
Article Title: PRP GENOTYPE AND AGENT EFFECTS IN SCRAPIE - CHANGE IN ALLELIC INTERACTION WITH DIFFERENT ISOLATES OF AGENT IN SHEEP, A NATURAL HOST OF SCRAPIE
Authors: Goldmann, W, Hunter, N, Smith, G, Foster, J, Hope, J
Journal: JOURNAL OF GENERAL VIROLOGY
Volume: 75
Page: 989-995
Year: 1994
Addresses: 
· AFRC, INST ANIM HLTH, OGSTON BLDG, W MAINS RD, MIDLOTHIAN, SCOTLAND
· MRC, NEUROPATHOGENESIS UNIT, EDINBURGH EH9 3JF, MIDLOTHIAN, SCOTLAND

***Article 18
Total Cites: 125
Article Title: GENETIC AND INFECTIOUS PRION DISEASES
Authors: Prusiner, SB
Journal: ARCHIVES OF NEUROLOGY
Volume: 50
Page: 1129-1153
Year: 1993
Addresses: 
· UNIV CALIF SAN FRANCISCO, DEPT NEUROL, HSE-781, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT BIOCHEM, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT BIOPHYS, SAN FRANCISCO, CA, USA

***Article 19
Total Cites: 123
Article Title: TRANSMISSION OF CREUTZFELDT-JAKOB-DISEASE FROM HUMANS TO TRANSGENIC MICE EXPRESSING CHIMERIC HUMAN-MOUSE PRION PROTEIN
Authors: Telling, GC, Scott, M, Hsiao, KK, Foster, D, Yang, SL, Torchia, M, Sidle, KCL, Collinge, J, Dearmond, SJ, Prusiner, SB
Journal: PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
Volume: 91
Page: 9936-9940
Year: 1994
Addresses: 
· UNIV CALIF SAN FRANCISCO, DEPT NEUROL, HSE-781, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT BIOCHEM & BIOPHYS, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT PATHOL, SAN FRANCISCO, CA, USA
· UNIV LONDON IMPERIAL COLL SCI TECHNOL & MED, ST MARYS HOSP, SCH MED, DEPT BIOCHEM & MOLEC GENET, LONDON W2 1PG, ENGLAND

***Article 20
Total Cites: 123
Article Title: NEW VARIANT CREUTZFELDT-JAKOB DISEASE: NEUROLOGICAL FEATURES AND DIAGNOSTIC TESTS
Authors: Zeidler, M, Stewart, GE, Barraclough, CR, Bateman, DE, Bates, D, Burn, DJ, Colchester, AC, Durward, W, Fletcher, NA, Hawkins, SA, Mackenzie, JM, Will, RG
Journal: LANCET
Volume: 350
Page: 903-907
Year: 1997
Addresses: 
· WESTERN GEN HOSP, NATL CREUTZFELDT JAKOB DIS SURVEILLANCE UNIT, EDINBURGH EH4 2XU, MIDLOTHIAN, SCOTLAND

ESI Special Topic of:
"Mad Cow & Other Prion Diseases," Published August 2003

•> Search Special Topics
Mad Cow & Other Prion Diseases Menu || All Topics Menu

Help || About || Contact

ScienceWatch.com - Tracking Trends and Perfomance in Basic Research
Go to the new ScienceWatch.com

Write to the Webmaster with questions/comments. Terms of Usage.
The Research Services Group of Thomson Scientific |
(c) 2008 The Thomson Corporation.