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***Article 1
Total Cites: 858
Article Title: A NEW VARIANT OF CREUTZFELDT-JAKOB DISEASE IN THE UK
Authors: Will, RG, Ironside, JW, Zeidler, M, Cousens, SN, Estibeiro, K, Alperovitch, A, Poser, S, Pocchiari, M, Hofman, A, Smith, PG
Journal: LANCET
Volume: 347
Page: 921-925
Year: 1996
Addresses:
· WESTERN GEN HOSP, NATL CJD SURVEILLANCE UNIT, EDINBURGH EH4 2XU, MIDLOTHIAN, SCOTLAND
· LONDON SCH HYG & TROP MED, DEPT EPIDEMIOL & POPULAT SCI, LONDON WC1, ENGLAND
· HOP LA PITIE SALPETRIERE, INSERM, PARIS, FRANCE
· UNIV GOTTINGEN, NEUROL KLIN & POLIKLIN, W-3400 GOTTINGEN, GERMANY
· IST SUPER SANITA, VIROL LAB, I-00161 ROME, ITALY
· ERASMUS UNIV ROTTERDAM, ROTTERDAM, NETHERLANDS
***Article 2
Total Cites: 564
Article Title: MOLECULAR ANALYSIS OF PRION STRAIN VARIATION AND THE AETIOLOGY OF 'NEW VARIANT' CJD
Authors: Collinge, J, Sidle, KCL, Meads, J, Ironside, J, Hill, AF
Journal: NATURE
Volume: 383
Page: 685-690
Year: 1996
Addresses:
· ST MARYS, IMPERIAL COLL SCH MED, DEPT BIOCHEM & MOL GENET, NEUROGENET UNIT, LONDON W2 1PG, ENGLAND
· WESTERN GEN HOSP, NATL CJD SURVEILLANCE UNIT, EDINBURGH EH4 2XU, MIDLOTHIAN, SCOTLAND
· ST MARYS HOSP, DEPT NEUROL, LONDON W2 1NY, ENGLAND
***Article 3
Total Cites: 540
Article Title: PRIONS
Authors: Prusiner, SB
Journal: PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
Volume: 95
Page: 13363-13383
Year: 1998
Addresses:
· Univ Calif San Francisco, Dept Neurol, San Francisco, CA, USA
· Univ Calif San Francisco, Dept Neurol, San Francisco, CA, USA
· Univ Calif San Francisco, Dept Biochem & Biophys, San Francisco, CA, USA
***Article 4
Total Cites: 496
Article Title: TRANSMISSIONS TO MICE INDICATE THAT 'NEW VARIANT' CJD IS CAUSED BY THE BSE AGENT
Authors: Bruce, ME, Will, RG, Ironside, JW, Mcconnell, I, Drummond, D, Suttie, A, Mccardle, L, Chree, A, Hope, J, Birkett, C, Cousens, S, Fraser, H, Bostock, CJ
Journal: NATURE
Volume: 389
Page: 498-501
Year: 1997
Addresses:
· INST ANIM HLTH, BBSRC MRC NEUROPATHOGENESIS UNIT, W MAINS RD, EDINBURGH EH9 3JF, MIDLOTHIAN, SCOTLAND
· WESTERN GEN HOSP, NATL CJD SURVEILLANCE UNIT, EDINBURGH EH4 2XU, MIDLOTHIAN, SCOTLAND
· INST ANIM HLTH, NEWBURY RG20 7NN, BERKS, ENGLAND
· UNIV LONDON LONDON SCH HYG & TROP MED, DEPT EPIDEMIOL & POPULAT SCI, LONDON WC1E 7HT, ENGLAND
***Article 5
Total Cites: 313
Article Title: PRION PROTEIN IS NECESSARY FOR NORMAL SYNAPTIC FUNCTION
Authors: Collinge, J, Whittington, MA, Sidle, KCL, Smith, CJ, Palmer, MS, Clarke, AR, Jefferys, JGR
Journal: NATURE
Volume: 370
Page: 295-297
Year: 1994
Addresses:
· ST MARYS HOSP, SCH MED, DEPT BIOCHEM & MOLEC GENET, PRION DIS GRP, LONDON W2 1PG, ENGLAND
· ST MARYS HOSP, SCH MED, DEPT PHYSIOL & BIOPHYS, LONDON W2 1PG, ENGLAND
· ST MARYS HOSP, DEPT NEUROL, LONDON W2 1NY, ENGLAND
· UNIV BRISTOL, SCH MED SCI, DEPT BIOCHEM, BRISTOL BS8 1TD, ENGLAND
***Article 6
Total Cites: 306
Article Title: NMR STRUCTURE OF THE MOUSE PRION PROTEIN DOMAIN PRP(121-231)
Authors: Riek, R, Hornemann, S, Wider, G, Billeter, M, Glockshuber, R, Wuthrich, K
Journal: NATURE
Volume: 382
Page: 180-182
Year: 1996
Addresses:
· ETH HONGGERBERG, INST MOLEK BIOL & BIOPHYS, CH-8093 ZURICH, SWITZERLAND
***Article 7
Total Cites: 305
Article Title: THE CELLULAR PRION PROTEIN BINDS COPPER IN VIVO
Authors: Brown, DR, Qin, KF, Herms, JW, Madlung, A, Manson, J, Strome, R, Fraser, PE, Kruck, T, Vonbohlen, A, Schulzschaeffer, W, Giese, A, Westaway, D, Kretzschmar, H
Journal: NATURE
Volume: 390
Page: 684-687
Year: 1997
Addresses:
· UNIV GOTTINGEN, DEPT NEUROPATHOL, D-37075 GOTTINGEN, GERMANY
· UNIV TORONTO, CTR RES NEURODEGENERAT DIS, TORONTO, ON M5S 3H2, CANADA
· UNIV TORONTO, DEPT LAB MED & PATHOBIOL, TORONTO, ON M5S 3H2, CANADA
· UNIV TORONTO, DEPT MED BIOPHYS, TORONTO, ON M5S 3H2, CANADA
· UNIV TORONTO, DEPT PHYSIOL, TORONTO, ON M5S 3H2, CANADA
· NEUROPATHOGENESIS UNIT, EDINBURGH EA 3TF, MIDLOTHIAN, SCOTLAND
· INST SPEKTROCHEM & ANGEW SPEKTROSKOPIE, D-44013 DORTMUND, GERMANY
***Article 8
Total Cites: 286
Article Title: PRION DISEASES AND THE BSE CRISIS
Authors: Prusiner, SB
Journal: SCIENCE
Volume: 278
Page: 245-251
Year: 1997
Addresses:
· UNIV CALIF SAN FRANCISCO, DEPT NEUROL, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT BIOCHEM & BIOPHYS, SAN FRANCISCO, CA, USA
***Article 9
Total Cites: 245
Article Title: TRANSMISSION DYNAMICS AND EPIDEMIOLOGY OF BSE IN BRITISH CATTLE
Authors: Anderson, RM, Donnelly, CA, Ferguson, NM, Woolhouse, MEJ, Watt, CJ, Udy, HJ, Mawhinney, S, Dunstan, SP, Southwood, TRE, Wilesmith, JW, Ryan, JBM, Hoinville, LJ, Hillerton, JE, Austin, AR, Wells, GAH
Journal: NATURE
Volume: 382
Page: 779-788
Year: 1996
Addresses:
· UNIV OXFORD, DEPT ZOOL, CTR EPIDEMIOL INFECT DIS, OXFORD OX1 3PS, ENGLAND
· UNIV COLORADO, HLTH SCI CTR, DEPT PREVENT MED & BIOMETR, DENVER, CO, USA
· CENT VET LAB, ADDLESTONE KT15 3NB, SURREY, ENGLAND
· INST ANIM HLTH, COMPTON NG20 7NN, BERKS, ENGLAND
***Article 10
Total Cites: 229
Article Title: ROLE OF MICROGLIA AND HOST PRION PROTEIN IN NEUROTOXICITY OF A PRION PROTEIN FRAGMENT
Authors: Brown, DR, Schmidt, B, Kretzschmar, HA
Journal: NATURE
Volume: 380
Page: 345-347
Year: 1996
Addresses:
· UNIV GOTTINGEN, INST NEUROPATHOL, D-37075 GOTTINGEN, GERMANY
· UNIV GOTTINGEN, ZENTRUM BIOCHEM & MOL ZELLBIOL, D-37075 GOTTINGEN, GERMANY
***Article 11
Total Cites: 206
Article Title: A CRUCIAL ROLE FOR B CELLS IN NEUROINVASIVE SCRAPIE
Authors: Klein, MA, Frigg, R, Flechsig, E, Raeber, AJ, Kalinke, U, Bluethmann, H, Bootz, F, Suter, M, Zinkernagel, RM, Aguzzi, A
Journal: NATURE
Volume: 390
Page: 687-690
Year: 1997
Addresses:
· UNIV ZURICH, INST NEUROPATHOL, CH-8091 ZURICH, SWITZERLAND
· UNIV ZURICH, INST MOL BIOL, CH-8091 ZURICH, SWITZERLAND
· UNIV ZURICH, INST EXPT IMMUNOL, CH-8091 ZURICH, SWITZERLAND
· HOFFMANN LA ROCHE AG, CH-4070 BASEL, SWITZERLAND
· UNIV ZURICH, INST LAB ANIM SCI, CH-8057 ZURICH, SWITZERLAND
***Article 12
Total Cites: 197
Article Title: TRANSMISSION OF BOVINE SPONGIFORM ENCEPHALOPATHY AND SCRAPIE TO MICE - STRAIN VARIATION AND THE SPECIES BARRIER
Authors: Bruce, M, Chree, A, Mcconnell, I, Foster, J, Pearson, G, Fraser, H
Journal: PHILOSOPHICAL TRANSACTIONS OF THE ROYAL SOCIETY OF LONDON SERIES B-BIOLOGICAL SCIENCES
Volume: 343
Page: 405-411
Year: 1994
Addresses:
· AFRC, INST ANIM HLTH, W MAINS RD, EDINBURGH EH9 3JF, MIDLOTHIAN, SCOTLAND
· MRC, NEUROPATHOGENESIS UNIT, EDINBURGH EH9 3JF, MIDLOTHIAN, SCOTLAND
· UNIV BRISTOL, SCH VET SCI, BRISTOL BS18 7DU, AVON, ENGLAND
***Article 13
Total Cites: 194
Article Title: INVESTIGATION OF VARIANT CREUTZFELDT-JAKOB DISEASE AND OTHER HUMAN PRION DISEASES WITH TONSIL BIOPSY SAMPLES
Authors: Hill, AF, Butterworth, RJ, Joiner, S, Jackson, G, Rossor, MN, Thomas, DJ, Frosh, A, Tolley, N, Bell, JE, Spencer, M, King, A, Al-sarraj, S, Ironside, JW, Lantos, PL, Collinge, J
Journal: LANCET
Volume: 353
Page: 183-189
Year: 1999
Addresses:
· St Marys Hosp, Imperial Coll Sch Med, Dept Neurogenet, Praed St, London W2 1PG, England
· St Marys Hosp, Imperial Coll Sch Med, Dept Neurogenet, London W2 1PG, England
· St Marys Hosp, Specialist Prion Dis Clin, London W2 1PG, England
· St Marys Hosp, Dept Neurol, London W2 1PG, England
· St Marys Hosp, Dept Ear Nose & Throat Surg, London W2 1PG, England
· Natl CJG Surveillance Unit, Edinburgh, Scotland
· Inst Psychiat, Dept Neuropathol, London, England
***Article 14
Total Cites: 171
Article Title: TRANSMISSION OF THE BSE AGENT TO MICE IN THE ABSENCE OF DETECTABLE ABNORMAL PRION PROTEIN
Authors: Lasmezas, CI, Deslys, JP, Robain, O, Jaegly, A, Beringue, V, Peyrin, JM, Fournier, JG, Hauw, JJ, Rossier, J, Dormont, D
Journal: SCIENCE
Volume: 275
Page: 402-405
Year: 1997
Addresses:
· CEA, SERV NEUROVIROL, DSV, DRM, F-92265 FONTENAY ROSES, FRANCE
· HOP ST VINCENT DE PAUL, INSERM, U29, F-75674 PARIS 14, FRANCE
· HOP LA PITIE SALPETRIERE, INSERM, U153, F-75651 PARIS 13, FRANCE
· HOP LA PITIE SALPETRIERE, INSERM, U360, LAB ESCOUROLLE, F-75651 PARIS 13, FRANCE
· ECOLE SUPER PHYS & CHIM IND VILLE PARIS, CNRS, URA 2054, F-75231 PARIS 5, FRANCE
***Article 15
Total Cites: 159
Article Title: PRION (PRPSC)-SPECIFIC EPITOPE DEFINED BY A MONOCLONAL ANTIBODY
Authors: Korth, C, Stierli, B, Streit, P, Moser, M, Schaller, O, Fischer, R, Schulzschaeffer, W, Kretzschmar, H, Raeber, A, Braun, U, Ehrensperger, F, Hornemann, S, Glockshuber, R, Riek, R, Billeter, M, Wuthrich, K, Oesch, B
Journal: NATURE
Volume: 390
Page: 74-77
Year: 1997
Addresses:
· UNIV ZURICH, PRION AG, WINTERTHURERSTR 190, CH-8057 ZURICH, SWITZERLAND
· UNIV ZURICH, BRAIN RES INST, CH-8029 ZURICH, SWITZERLAND
· ETH ZURICH, INST BIOCHEM, CH-8092 ZURICH, SWITZERLAND
· UNIV GOTTINGEN, INST NEUROPATHOL, D-37075 GOTTINGEN, GERMANY
· UNIV ZURICH, INST NEUROPATHOL, CH-8091 ZURICH, SWITZERLAND
· UNIV ZURICH, KLIN WIEDERKAUER & PFERDEMED, CH-8057 ZURICH, SWITZERLAND
· UNIV ZURICH, INST VET PATHOL, CH-8057 ZURICH, SWITZERLAND
· ETH ZURICH, INST MOL BIOL & BIOPHYS, CH-8093 ZURICH, SWITZERLAND
***Article 16
Total Cites: 149
Article Title: HUMAN PRION DISEASES
Authors: Prusiner, SB, Hsiao, KK
Journal: ANNALS OF NEUROLOGY
Volume: 35
Page: 385-395
Year: 1994
Addresses:
· UNIV CALIF SAN FRANCISCO, DEPT NEUROL, HSE 781, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT BIOCHEM & BIOPHYS, SAN FRANCISCO, CA, USA
· UNIV MINNESOTA, DEPT NEUROL, MINNEAPOLIS, MN, USA
***Article 17
Total Cites: 140
Article Title: PRP GENOTYPE AND AGENT EFFECTS IN SCRAPIE - CHANGE IN ALLELIC INTERACTION WITH DIFFERENT ISOLATES OF AGENT IN SHEEP, A NATURAL HOST OF SCRAPIE
Authors: Goldmann, W, Hunter, N, Smith, G, Foster, J, Hope, J
Journal: JOURNAL OF GENERAL VIROLOGY
Volume: 75
Page: 989-995
Year: 1994
Addresses:
· AFRC, INST ANIM HLTH, OGSTON BLDG, W MAINS RD, MIDLOTHIAN, SCOTLAND
· MRC, NEUROPATHOGENESIS UNIT, EDINBURGH EH9 3JF, MIDLOTHIAN, SCOTLAND
***Article 18
Total Cites: 125
Article Title: GENETIC AND INFECTIOUS PRION DISEASES
Authors: Prusiner, SB
Journal: ARCHIVES OF NEUROLOGY
Volume: 50
Page: 1129-1153
Year: 1993
Addresses:
· UNIV CALIF SAN FRANCISCO, DEPT NEUROL, HSE-781, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT BIOCHEM, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT BIOPHYS, SAN FRANCISCO, CA, USA
***Article 19
Total Cites: 123
Article Title: TRANSMISSION OF CREUTZFELDT-JAKOB-DISEASE FROM HUMANS TO TRANSGENIC MICE EXPRESSING CHIMERIC HUMAN-MOUSE PRION PROTEIN
Authors: Telling, GC, Scott, M, Hsiao, KK, Foster, D, Yang, SL, Torchia, M, Sidle, KCL, Collinge, J, Dearmond, SJ, Prusiner, SB
Journal: PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
Volume: 91
Page: 9936-9940
Year: 1994
Addresses:
· UNIV CALIF SAN FRANCISCO, DEPT NEUROL, HSE-781, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT BIOCHEM & BIOPHYS, SAN FRANCISCO, CA, USA
· UNIV CALIF SAN FRANCISCO, DEPT PATHOL, SAN FRANCISCO, CA, USA
· UNIV LONDON IMPERIAL COLL SCI TECHNOL & MED, ST MARYS HOSP, SCH MED, DEPT BIOCHEM & MOLEC GENET, LONDON W2 1PG, ENGLAND
***Article 20
Total Cites: 123
Article Title: NEW VARIANT CREUTZFELDT-JAKOB DISEASE: NEUROLOGICAL FEATURES AND DIAGNOSTIC TESTS
Authors: Zeidler, M, Stewart, GE, Barraclough, CR, Bateman, DE, Bates, D, Burn, DJ, Colchester, AC, Durward, W, Fletcher, NA, Hawkins, SA, Mackenzie, JM, Will, RG
Journal: LANCET
Volume: 350
Page: 903-907
Year: 1997
Addresses:
· WESTERN GEN HOSP, NATL CREUTZFELDT JAKOB DIS SURVEILLANCE UNIT, EDINBURGH EH4 2XU, MIDLOTHIAN, SCOTLAND
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